low-grade fibromyxoid sarcoma

GPTKB entity

Statements (25)
Predicate Object
gptkbp:instanceOf gptkb:rhabdomyosarcoma
soft tissue tumor
gptkbp:affects young adults
middle-aged adults
gptkbp:canBeMalignant true
gptkbp:firstDescribed 1987
G. A. Evans
gptkbp:hasGeneticAlteration FUS-CREB3L1 fusion
FUS-CREB3L2 fusion
gptkbp:hasICD-OCode 8818/3
gptkbp:hasImmunohistochemistryMarker MUC4 positive
gptkbp:hasMetastasisRisk moderate
gptkbp:hasRecurrenceRisk high
gptkbp:histology fibrous tissue
myxoid tissue
https://www.w3.org/2000/01/rdf-schema#label low-grade fibromyxoid sarcoma
gptkbp:location trunk
deep soft tissues
proximal extremities
gptkbp:prognosis indolent clinical course
potential for late metastasis
gptkbp:synonym Evans tumor
gptkbp:treatment surgical excision
gptkbp:bfsParent gptkb:CREB3L2
gptkbp:bfsLayer 7