desmoplastic small round cell tumor
GPTKB entity
Statements (23)
| Predicate | Object |
|---|---|
| gptkbp:instanceOf |
gptkb:rhabdomyosarcoma
rare cancer |
| gptkbp:affects |
children
young adults |
| gptkbp:firstDescribed |
1989
William Gerald |
| gptkbp:hasGeneticAlteration |
EWSR1-WT1 fusion
|
| gptkbp:histology |
small round blue cells
|
| https://www.w3.org/2000/01/rdf-schema#label |
desmoplastic small round cell tumor
|
| gptkbp:ICD-10_code |
C49.A
|
| gptkbp:incidence |
<1 per million per year
|
| gptkbp:location |
abdomen
|
| gptkbp:marking |
gptkb:EMA
gptkb:desmin gptkb:WT1 cytokeratin |
| gptkbp:prognosis |
poor
|
| gptkbp:synonym |
DSRCT
|
| gptkbp:treatment |
surgery
radiation therapy chemotherapy |
| gptkbp:bfsParent |
gptkb:EWSR1
|
| gptkbp:bfsLayer |
7
|