Systemic Capillary Leak Syndrome
GPTKB entity
Statements (32)
| Predicate | Object |
|---|---|
| gptkbp:instanceOf |
medical condition
rare disease |
| gptkbp:affects |
adults
children |
| gptkbp:alsoKnownAs |
Clarkson disease
|
| gptkbp:associatedWith |
monoclonal gammopathy
|
| gptkbp:causedBy |
leakage of plasma from capillaries into surrounding tissues
|
| gptkbp:characterizedBy |
edema
hypoalbuminemia hemoconcentration recurrent episodes of severe hypotension |
| gptkbp:complication |
death
multi-organ failure |
| gptkbp:diagnosedBy |
clinical presentation
laboratory findings |
| gptkbp:firstDescribed |
1960
Dr. Bayard Clarkson |
| https://www.w3.org/2000/01/rdf-schema#label |
Systemic Capillary Leak Syndrome
|
| gptkbp:ICD-10_code |
R60.1
|
| gptkbp:incidence |
extremely rare
|
| gptkbp:prognosis |
variable
|
| gptkbp:symptom |
shock
organ dysfunction swelling low blood pressure |
| gptkbp:treatment |
gptkb:theophylline
gptkb:IVIG vasopressors intravenous fluids terbutaline |
| gptkbp:bfsParent |
gptkb:SCLS
|
| gptkbp:bfsLayer |
7
|