Primary Sclerosing Peritonitis Syndrome

GPTKB entity

Statements (17)
Predicate Object
gptkbp:instanceOf gptkb:disease
gptkbp:affects peritoneum
gptkbp:alternativeName Abdominal Cocoon Syndrome
Sclerosing Encapsulating Peritonitis
gptkbp:causedBy idiopathic
gptkbp:complication gptkb:bowel_obstruction
malnutrition
gptkbp:hasEpidemiology rare
https://www.w3.org/2000/01/rdf-schema#label Primary Sclerosing Peritonitis Syndrome
gptkbp:symptom abdominal pain
abdominal distension
ascites
gptkbp:treatment immunosuppressive therapy
corticosteroids
surgical intervention
gptkbp:bfsParent gptkb:PSPS
gptkbp:bfsLayer 8