Lamb-Shaffer syndrome

GPTKB entity

Statements (24)
Predicate Object
gptkbp:instanceOf gptkb:genetic_disorder
gptkb:rare_disease
gptkbp:affects gptkb:nervous_system
development
gptkbp:diagnosedBy genetic testing
gptkbp:firstDescribed 2012
gptkbp:hasOrphanetID ORPHA:404447
gptkbp:ICD-10_code Q87.8
gptkbp:inheritance autosomal dominant
gptkbp:mutationAssociatedWith SOX5 gene
gptkbp:namedAfter Annie Lamb
Lisa Shaffer
gptkbp:OMIM 616803
gptkbp:prevalence very rare
gptkbp:symptom gptkb:intellectual_disability
hypotonia
developmental delay
distinctive facial features
speech delay
behavioral problems
autistic features
gptkbp:bfsParent gptkb:SOX5
gptkbp:bfsLayer 7
https://www.w3.org/2000/01/rdf-schema#label Lamb-Shaffer syndrome