Kabuki syndrome type 1

GPTKB entity

Statements (53)
Predicate Object
gptkbp:instanceOf gptkb:genetic_disorder
gptkbp:causedBy mutation in KMT2D gene
gptkbp:complication gptkb:autism_spectrum_disorder
gptkb:malocclusion
gptkb:brachydactyly
gptkb:strabismus
congenital heart defects
hypotonia
scoliosis
vision problems
hearing loss
seizures
recurrent infections
microcephaly
renal anomalies
gastrointestinal anomalies
clinodactyly
dental anomalies
epicanthal folds
feeding difficulties
joint laxity
ptosis
cleft palate
behavioral problems
hypodontia
arched eyebrows
delayed speech development
growth hormone deficiency
delayed motor development
endocrine abnormalities
hip dislocation
depressed nasal tip
large, prominent earlobes
long palpebral fissures
persistent fingertip pads
vertebral anomalies
gptkbp:containsGene gptkb:KMT2D
gptkbp:frequency 1 in 32,000 births
gptkbp:inheritance autosomal dominant
gptkbp:OMIM 147920
gptkbp:onset congenital
gptkbp:prevalence rare
gptkbp:symptom gptkb:intellectual_disability
short stature
skeletal abnormalities
distinctive facial features
cardiac anomalies
immunological defects
gptkbp:synonym Niikawa-Kuroki syndrome
gptkbp:treatment supportive care
gptkbp:bfsParent gptkb:KMT2D
gptkbp:bfsLayer 7
https://www.w3.org/2000/01/rdf-schema#label Kabuki syndrome type 1