HSAN type V

GPTKB entity

Statements (23)
Predicate Object
gptkbp:instanceOf gptkb:genetic_disorder
gptkb:hereditary_sensory_and_autonomic_neuropathy
gptkbp:alsoKnownAs Hereditary Sensory and Autonomic Neuropathy type V
Congenital insensitivity to pain with partial anhidrosis
gptkbp:diagnosedBy genetic testing
gptkbp:differentialDiagnosis gptkb:HSAN_type_IV
congenital insensitivity to pain without anhidrosis
gptkbp:firstDescribed 2004
gptkbp:inheritance autosomal recessive
gptkbp:mutationAssociatedWith NGF gene
gptkbp:OMIM 608654
gptkbp:onset congenital
gptkbp:prevalence rare
gptkbp:symptom insensitivity to pain
bone fractures
ulcerations
partial anhidrosis
recurrent injuries
gptkbp:treatment supportive care
injury prevention
gptkbp:bfsParent gptkb:Hereditary_Sensory_and_Autonomic_Neuropathy
gptkbp:bfsLayer 9
https://www.w3.org/2000/01/rdf-schema#label HSAN type V