Edwards syndrome

GPTKB entity

Statements (34)
Predicate Object
gptkbp:instanceOf gptkb:genetic_disorder
gptkbp:affects both males and females
gptkbp:alsoKnownAs trisomy 18
gptkbp:causedBy extra chromosome 18
gptkbp:chromosomeAffected gptkb:chromosome_18
gptkbp:commonIn females
gptkbp:diagnosedBy prenatal screening
karyotyping
gptkbp:firstDescribed gptkb:John_H._Edwards
1960
gptkbp:hasPartialForm mosaic trisomy 18
partial trisomy 18
gptkbp:ICD-10_code Q91.0-Q91.3
gptkbp:inheritance not inherited
gptkbp:medianSurvival few weeks to months
gptkbp:MeSH_ID D004537
gptkbp:OMIM 192500
gptkbp:percentageSurviving1Year less than 10%
gptkbp:prevalence 1 in 5,000 live births
gptkbp:prognosis poor
gptkbp:riskFactor advanced maternal age
gptkbp:symptom gptkb:intellectual_disability
congenital heart defects
low birth weight
small head
micrognathia
kidney malformations
clenched fists with overlapping fingers
rocker-bottom feet
gptkbp:treatment supportive care
gptkbp:bfsParent gptkb:chromosome_18
gptkb:John_H._Edwards
gptkbp:bfsLayer 7
https://www.w3.org/2000/01/rdf-schema#label Edwards syndrome