Behçet's disease

E654529

Behçet's disease is a rare, chronic inflammatory disorder characterized by recurrent mouth and genital ulcers, eye inflammation, and systemic vasculitis affecting multiple organ systems.

All labels observed (3)

Label Occurrences
Behçet's disease canonical 7
Behçet disease 1
Behçet syndrome 1

How this entity was disambiguated

Statements (63)

Predicate Object
instanceOf autoimmune disease
multisystem inflammatory disorder
affectsSystem arterial system
cardiovascular system
central nervous system
gastrointestinal tract
mucocutaneous system
musculoskeletal system
ocular system
venous system
associatedWith environmental triggers
genetic predisposition
immune dysregulation
canCauseComplication arterial aneurysm
canCauseComplication intestinal perforation
neurological disability
venous thrombosis
vision loss
diagnosedBy clinical criteria
epidemiology more prevalent along the ancient Silk Road
hasCause unknown etiology
hasClassificationCriteria International Criteria for Behçet's Disease
International Study Group criteria
hasCourse relapsing-remitting
hasDiagnosticTest pathergy test
hasHighPrevalenceIn East Asia
Middle East
Turkey
hasOnsetPattern chronic
hasPathology neutrophilic inflammation
systemic vasculitis
hasPrimarySymptom recurrent genital ulcers
recurrent oral aphthous ulcers
hasPrognosis variable
hasSymptom arthralgia
arthritis
blurred vision
erythema nodosum-like lesions
eye pain
eye redness
fatigue
fever
gastrointestinal ulceration
neurological involvement
papulopustular lesions
retinal vasculitis
skin lesions
uveitis
vascular thrombosis
hasSynonym Adamantiades–Behçet disease
Behçet syndrome
linked to: Behçet's disease
moreCommonIn young adults
namedAfter Hulusi Behçet
requiresFollowUp long-term monitoring
stronglyAssociatedWith HLA-B51 allele
treatedWith TNF-alpha inhibitors
linked to: Humira

apremilast
azathioprine
colchicine
corticosteroids
cyclophosphamide
cyclosporine
interferon-alpha

How these facts were elicited

Referenced by (9)

Full triples — surface form annotated when it differs from this entity's canonical label.

Hulusi Behçet eponymOf Behçet's disease
subject linked to: Ord. Prof. Dr. Hulusi Behçet
Hulusi Behçet hasAssociatedDisease Behçet's disease
subject linked to: Ord. Prof. Dr. Hulusi Behçet
Hulusi Behçet knownFor Behçet's disease
subject linked to: Hulusi
Hulusi Behçet hasDiscovered Behçet's disease
subject linked to: Hulusi
Hulusi Behçet eponymOf Behçet's disease
subject linked to: Hulusi
Behçet hasEponymousDisease Behçet's disease
Behçet's disease hasSynonym Behçet syndrome
linked to: Behçet's disease
Hulusi Behcet hasEponym Behçet's disease
erythema nodosum associatedWith Behçet disease
linked to: Behçet's disease