Dandy–Walker syndrome

GPTKB entity

Statements (50)
Predicate Object
gptkbp:instanceOf gptkb:genetic_disorder
gptkb:neurological_disorder
gptkbp:affects gptkb:cerebellum
fourth ventricle
posterior fossa
gptkbp:causedBy genetic factors
environmental factors
gptkbp:complication gptkb:intellectual_disability
muscle stiffness
paralysis
vision problems
hearing loss
seizures
gptkbp:diagnosedBy gptkb:CT_scan
MRI
ultrasound
gptkbp:firstDescribed gptkb:Walter_Dandy
gptkb:Arthur_Earl_Walker
1914
gptkbp:hasRelatedDisorder gptkb:Joubert_syndrome
Arnold–Chiari malformation
gptkbp:ICD-10_code Q03.1
gptkbp:inheritance autosomal dominant
autosomal recessive
sporadic
gptkbp:MeSH_ID D003616
gptkbp:namedAfter gptkb:Walter_Dandy
gptkb:Arthur_Earl_Walker
gptkbp:OMIM 220219
gptkbp:prevalence 1 in 25,000 to 35,000 live births
gptkbp:riskFactor chromosomal abnormalities
congenital infections
maternal diabetes
gptkbp:symptom gptkb:intellectual_disability
hydrocephalus
developmental delay
increased intracranial pressure
cyst formation near the base of the skull
enlarged fourth ventricle
partial or complete absence of cerebellar vermis
problems with movement
gptkbp:synonym Dandy–Walker malformation
Dandy–Walker complex
Dandy–Walker cyst
gptkbp:treatment occupational therapy
physical therapy
surgical shunt
gptkbp:bfsParent gptkb:Arthur_Earl_Walker
gptkbp:bfsLayer 8
https://www.w3.org/2000/01/rdf-schema#label Dandy–Walker syndrome